Brachydactyly-short stature-retinitis pigmentosa syndrome

Orpha code: 166035OMIM code: 250410

Definicja

Brachydactyly-short stature-retinitis pigmentosa syndrome is a rare, genetic, congenital limb malformation syndrome characterized by mild to severe short stature, brachydactyly, and retinal degeneration (usually retinitis pigmentosa), associated with variable intellectual disability, developmental delays, and craniofacial anomalies.

Disease data
Klasyfikacja

Malformation syndrome

Kod ORPHA
166035
Kod OMIM
250410
Kod ICD10
Q87.8
Kod ICD11
-

No additional description.

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