Multiple epiphyseal dysplasia, Beighton type

Orpha code: 166011OMIM code: 132450

Definicja

A rare primary bone dysplasia characterized by the association of multiple epiphyseal dysplasia, visual impairment (with early-onset progressive myopia, retinal thinning, and cataracts), and conductive hearing loss. Patients are of short stature and present brachydactyly, genu valgus deformity, and joint pain.

Disease data
Klasyfikacja

Disease

Synonimy
Multiple epiphyseal dysplasia-myopia-deafness syndrome
Dysplazja wielonasadowa - miopia - głuchota
Multiple epiphyseal dysplasia-myopia-hearing loss syndrome
Kod ORPHA
166011
Kod OMIM
132450
Kod ICD10
Q77.3
Kod ICD11
LD24.61

No additional description.

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