Multiple epiphyseal dysplasia, Beighton type

Orpha code: 166011OMIM code: 132450

Definition

A rare primary bone dysplasia characterized by the association of multiple epiphyseal dysplasia, visual impairment (with early-onset progressive myopia, retinal thinning, and cataracts), and conductive hearing loss. Patients are of short stature and present brachydactyly, genu valgus deformity, and joint pain.

Disease data
Classification

Disease

Synonyms
Multiple epiphyseal dysplasia-myopia-deafness syndrome
Dysplazja wielonasadowa - miopia - głuchota
Multiple epiphyseal dysplasia-myopia-hearing loss syndrome
ORPHA code
166011
OMIM code
132450
ICD10 code
Q77.3
ICD11 code
LD24.61

No additional description.

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