CNTNAP2-related developmental and epileptic encephalopathy

Orpha code: 163681OMIM code: 610042

Definicja

A rare, genetic, syndromic neurodevelopmental disorder characterized by moderate to mostly severe intellectual disability, speech impairment with normal or mildly delayed motor development and early-onset seizures often accompanied by developmental regression. Autistic behavior and stereotypic movements are common.

Disease data
Klasyfikacja

Disease

Synonimy
CDFE syndrome
CDFES
CNTNAP2-related DEE
Cortical dysplasia-focal epilepsy syndrome
Kod ORPHA
163681
Kod OMIM
610042
Kod ICD10
Q04.8
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl