CNTNAP2-related developmental and epileptic encephalopathy

Orpha code: 163681OMIM code: 610042

Definition

A rare, genetic, syndromic neurodevelopmental disorder characterized by moderate to mostly severe intellectual disability, speech impairment with normal or mildly delayed motor development and early-onset seizures often accompanied by developmental regression. Autistic behavior and stereotypic movements are common.

Disease data
Classification

Disease

Synonyms
CDFE syndrome
CDFES
CNTNAP2-related DEE
Cortical dysplasia-focal epilepsy syndrome
ORPHA code
163681
OMIM code
610042
ICD10 code
Q04.8
ICD11 code
-

No additional description.

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