Arthrogryposis-hyperkeratosis syndrome, lethal form

Orpha code: 1485OMIM code: 208158

Definicja

A rare arthrogryposis syndrome characterized by the association of multiple congenital joint contractures (of the large joints, fingers and toes) and hyperkeratosis (i.e. thick, scaling and fissured skin), with death occurring in early infancy. There have been no further reports in the literature since 1993.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Johnston-Aarons-Schelley syndrome
Zespół Johnstona, Aaronsa i Schelley
Kod ORPHA
1485
Kod OMIM
208158
Kod ICD10
Q68.8
Kod ICD11
-

No additional description.

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