Atrial septal defect-atrioventricular conduction defects syndrome

Definition

An extremely rare genetic congenital heart disease characterized by the presence of atrial septal defect, mostly of the ostium secundum type, associated with conduction anomalies like atrioventricular block, atrial fibrillation or right bundle branch block.

Disease data

Classification

Malformation syndrome

ORPHA code

1479

OMIM code

108900

ICD10 code

Q21.1

ICD11 code

*Soruce