Choroidal atrophy-alopecia syndrome

Orpha code: 1433OMIM code:

Definition

A rare ectodermal dysplasia syndrome, characterized by the association of choroidal atrophy (sometimes regional), together with other ectodermal dysplasia features including fine and sparse hair, absent or decreased lashes and eyebrows, and possibly mild visual loss and dysplastic/thick/grooved nails.

Disease data
Classification

Malformation syndrome

Synonyms
Moloney syndrome
Miejscowa atrofia błony naczyniowej i łysienie
Zespół Moloney'a
Regional choroidal atrophy and alopecia
ORPHA code
1433
OMIM code
-
ICD10 code
Q82.8
ICD11 code
LD27.0Y

No additional description.

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