Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare developmental defect during embryogenesis characterized by multifocal dilated lymphatic vessels involving multiple organs and tissues. Patients mostly present in infancy and childhood. Clinical course and prognosis depend on the affected sites and extent of the condition, deterioration of lung function being a major cause of morbidity and mortality. Disease data Classification Malformation syndrome Synonyms Diffuse lymphangioma GLA Limfangiomatoza rozlana Limfangiomatoza rozsiana Rozlany obrzęk limfatyczny Rozsiana malformacja limfatyczna Rozsiany obrzęk limfatyczny Uogólniona anomalia limfatyczna Diffuse lymphangiomatosis Disseminated lymphangioma Disseminated lymphangiomatosis Disseminated lymphatic malformation GLA Generalized lymphatic anomaly ORPHA code 141209 OMIM code - ICD10 code I89.8 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl