Cataract-deafness-hypogonadism syndrome

Orpha code: 1383OMIM code:

Definition

Cataract-deafness-hypogonadism syndrome is an extremely rare multiple congenital abnormality syndrome, described in only three brothers to date, that is characterized by the association of congenital cataract, sensorineural deafness, hypogonadism, mild intellectual deficit, hypertrichosis, and short stature. There have been no further descriptions in the literature since 1995.

Disease data
Classification

Malformation syndrome

Synonyms
Cataract-hearing loss-hypogonadism syndrome
Zespół Schaapa, Taylora i Baraitsera
Schaap-Taylor-Baraitser syndrome
ORPHA code
1383
OMIM code
-
ICD10 code
Q87.8
ICD11 code
LD2H.Y

No additional description.

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