Laryngotracheal angioma

Orpha code: 137935OMIM code:

Definition

A rare benign vascular tumor characterized by rapid growth after birth (followed by spontaneous partial regression over the course of years), potentially leading to life-threatening airway obstruction due to the subglottic location. Patients present with respiratory symptoms including biphasic stridor, recurrent croup, cyanosis, apnea, and sternal and intercostal retractions. The tumor may be accompanied by cutaneous hemangiomata, especially in the lower facial ("beard") distribution.

Disease data
Classification

Disease

ORPHA code
137935
OMIM code
-
ICD10 code
D18.0
ICD11 code
-

No additional description.

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