Naczyniak krtaniowo-tchawiczy

Kod Orpha: 137935Kod OMIM:

Definicja

A rare benign vascular tumor characterized by rapid growth after birth (followed by spontaneous partial regression over the course of years), potentially leading to life-threatening airway obstruction due to the subglottic location. Patients present with respiratory symptoms including biphasic stridor, recurrent croup, cyanosis, apnea, and sternal and intercostal retractions. The tumor may be accompanied by cutaneous hemangiomata, especially in the lower facial ("beard") distribution.

Dane
Klasyfikacja

Choroba

Kod ORPHA
137935
Kod OMIM
-
Kod ICD10
D18.0
Kod ICD11
-

Brak opisu rozszerzonego dla tej choroby. Opracowanie w toku.

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