Leukoencephalopathy with brain stem and spinal cord involvement-high lactate syndrome

Orpha code: 137898OMIM code: 611105

Definition

This disease is characterised by progressive cerebellar ataxia with pyramidal and spinal cord dysfunction, associated with distinctive MRI anomalies and increased lactate in the abnormal white matter.

Disease data
Classification

Disease

Synonyms
LBSL
LBSL
Leukoencephalopathy with brain stem and spinal cord involvement-lactate elevation syndrome
ORPHA code
137898
OMIM code
611105
ICD10 code
E88.8
ICD11 code
-

No additional description.

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