Medullary sponge kidney

Orpha code: 1309OMIM code:

Definicja

A rare renal tract malformation characterized by dilated malformation of the medullary collecting ducts (typically bilateral), and associated with stone formation, renal colic, hematuria, urinary tract infection, nephrocalcinosis, calcium nephrolithiasis, pyelonephritis, hypercalciuria and hypocitraturia. The disease is associated with abnormal distal tubular functions.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Cacchi-Ricci disease
Choroba Cacchi i Ricciego
MSK
MSK
Precalicial canalicular ectasia
Kod ORPHA
1309
Kod OMIM
-
Kod ICD10
Q61.5
Kod ICD11
LB30.8

No additional description.

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