Medullary sponge kidney

Orpha code: 1309OMIM code:

Definition

A rare renal tract malformation characterized by dilated malformation of the medullary collecting ducts (typically bilateral), and associated with stone formation, renal colic, hematuria, urinary tract infection, nephrocalcinosis, calcium nephrolithiasis, pyelonephritis, hypercalciuria and hypocitraturia. The disease is associated with abnormal distal tubular functions.

Disease data
Classification

Morphological anomaly

Synonyms
Cacchi-Ricci disease
Choroba Cacchi i Ricciego
MSK
MSK
Precalicial canalicular ectasia
ORPHA code
1309
OMIM code
-
ICD10 code
Q61.5
ICD11 code
LB30.8

No additional description.

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