TMEM70-related mitochondrial encephalo-cardio-myopathy

Orpha code: 1194OMIM code: 614052

Definicja

Mitochondrial encephalo-cardio-myopathy due to <i>TMEM70</i> mutation is characterized by early neonatal onset of hypotonia, hypetrophic cardiomyopathy and apneic spells within hours after birth accompanied by lactic acidosis, hyperammonemia and 3-methylglutaconic aciduria.

Disease data
Klasyfikacja

Disease

Synonimy
Mitochondrial encephalo-cardio-myopathy due to F1Fo ATPase deficiency
Mitochondrialna encefalo-kardio-miopatia z powodu niedoboru F1Fo ATP-azy
Mitochondrialna encefalo-kardio-miopatia z powodu niedoboru kompleksu V mitochondrialnego łańcucha oddechowego
Mitochondrialna encefalo-kardio-miopatia z powodu niedoboru syntazy ATP
Mitochondrial encephalo-cardio-myopathy due to isolated ATP synthase deficiency
Mitochondrial encephalo-cardio-myopathy due to isolated mitochondrial respiratory chain complex V deficiency
Kod ORPHA
1194
Kod OMIM
614052
Kod ICD10
G71.3
Kod ICD11
-

No additional description.

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