Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Ulnar hypoplasia-split foot syndrome is characterised by the association of severe ulnar hypoplasia, absence of fingers two to five, and split-foot. It has been described in four males belonging to two generations of the same family. X-linked recessive inheritance is suggested, but autosomal dominant transmission cannot be excluded. Disease data Classification Malformation syndrome Synonyms Ulnar hypoplasia-lobster-claw deformity of feet syndrome Hipoplazja kości łokciowej - deformacja stóp typu szczypce homara Zespół Van den Berghe i Dequeckera Van den Berghe-Dequecker syndrome ORPHA code 1122 OMIM code 314360 ICD10 code Q73.8 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl