Autosomal recessive spastic paraplegia type 27

Orpha code: 101007OMIM code: 609041

Definicja

Autosomal recessive spastic paraplegia type 27 is a rare, pure or complex hereditary spastic paraplegia characterized by a variable onset of slowly progressive lower limb spasticity, hyperreflexia and extensor plantar responses, that may be associated with sensorimotor polyneuropathy, decreased vibration sense, lower limb distal muscle wasting, dysarthria and mild to moderate intellectual disability.

Disease data
Klasyfikacja

Disease

Synonimy
SPG27
SPG27
Kod ORPHA
101007
Kod OMIM
609041
Kod ICD10
G11.4
Kod ICD11
-

No additional description.

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