Refractory anemia with excess blasts type 2

Orpha code: 100020OMIM code:

Definition

A very severe type of RAEB characterized by cytopenias and the following hematological parameters: uni- or multilineage dysplasia, 10% to 19% blasts in bone marrow or 5% to 19% in peripheral blood, variable presence of Auer rods (abnormal, needle-shaped or round inclusions in the cytoplasm of myeloblasts and promyelocytes). Median survival has been reported to be 18 months.

Disease data
Classification

Clinical subtype

Synonyms
RAEB-2
RAEB-2
ORPHA code
100020
OMIM code
-
ICD10 code
D46.2
ICD11 code
-

No additional description.

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