Refractory anemia with excess blasts type 1

Orpha code: 100019OMIM code:

Definition

A severe type of RAEB characterized by cytopenias and the following hematological parameters: uni- or multilineage dysplasia, 5% to 9% blasts in bone marrow or 2% to 4% in peripheral blood, and no Auer rods (abnormal, needle-shaped or round inclusions in the cytoplasm of myeloblasts and promyelocytes). Median survival has been reported to be 18 months.

Disease data
Classification

Clinical subtype

Synonyms
RAEB-1
RAEB-1
ORPHA code
100019
OMIM code
-
ICD10 code
D46.2
ICD11 code
-

No additional description.

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