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Kod Orpha: 477742Kod OMIM:

Definicja

A rare soft tissue tumor characterized by a solitary mass-forming fibrous proliferation that usually occurs in the subcutaneous tissue, composed of uniform fibroblastic/myofibroblastic cells displaying a loose growth pattern. Upper extremities, trunk, and head and neck are most frequently affected. The lesion typically grows rapidly and almost always measures less than five centimeters in diameter. Macroscopically, it may appear circumscribed or infiltrative but is not encapsulated. Recurrence after excision is very rare, and metastasis does not occur.

Dane
Klasyfikacja

Choroba

Synonimy
Pseudosarcomatous fasciitis
Pseudosarcomatous fibromatosis
Pseudosarcomatous fasciitis
Pseudosarcomatous fibromatosis
Kod ORPHA
477742
Kod OMIM
-
Kod ICD10
M79.8
Kod ICD11
-

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