Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare soft tissue tumor characterized by a solitary mass-forming fibrous proliferation that usually occurs in the subcutaneous tissue, composed of uniform fibroblastic/myofibroblastic cells displaying a loose growth pattern. Upper extremities, trunk, and head and neck are most frequently affected. The lesion typically grows rapidly and almost always measures less than five centimeters in diameter. Macroscopically, it may appear circumscribed or infiltrative but is not encapsulated. Recurrence after excision is very rare, and metastasis does not occur. Disease data Klasyfikacja Disease Synonimy Pseudosarcomatous fasciitis Pseudosarcomatous fibromatosis Pseudosarcomatous fasciitis Pseudosarcomatous fibromatosis Kod ORPHA 477742 Kod OMIM - Kod ICD10 - Kod ICD11 - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl