Zespół Sweeta

Kod Orpha: 3243Kod OMIM: 608068

Definicja

A rare inflammatory disease characterized by abrupt appearance of painful, edematous and erythematous papules, plaques and nodules on the skin, and frequently accompanied by fever and neutrophilia with a dense infiltration of mature neutrophils that are typically located in the upper dermis. The disease is classically associated with inflammatory disease, pregnancy, infection (mostly of the upper respiratory tract), or vaccination but may be idiopathic, associated with a hematological or visceral malignancy, or drug-induced.

Dane
Klasyfikacja

Choroba

Synonimy
Acute febrile neutrophilic dermatosis
Ostra neutrofilowa dermatoza gorączkowa
Kod ORPHA
3243
Kod OMIM
608068
Kod ICD10
L98.2
Kod ICD11
EB20

Brak opisu rozszerzonego dla tej choroby. Opracowanie w toku.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl