Sweet syndrome

Orpha code: 3243OMIM code: 608068

Definition

A rare inflammatory disease characterized by abrupt appearance of painful, edematous and erythematous papules, plaques and nodules on the skin, and frequently accompanied by fever and neutrophilia with a dense infiltration of mature neutrophils that are typically located in the upper dermis. The disease is classically associated with inflammatory disease, pregnancy, infection (mostly of the upper respiratory tract), or vaccination but may be idiopathic, associated with a hematological or visceral malignancy, or drug-induced.

Disease data
Classification

Disease

Synonyms
Acute febrile neutrophilic dermatosis
Ostra neutrofilowa dermatoza gorączkowa
ORPHA code
3243
OMIM code
608068
ICD10 code
L98.2
ICD11 code
EB20

No additional description.

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