Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare inflammatory disease characterized by abrupt appearance of painful, edematous and erythematous papules, plaques and nodules on the skin, and frequently accompanied by fever and neutrophilia with a dense infiltration of mature neutrophils that are typically located in the upper dermis. The disease is classically associated with inflammatory disease, pregnancy, infection (mostly of the upper respiratory tract), or vaccination but may be idiopathic, associated with a hematological or visceral malignancy, or drug-induced. Disease data Classification Disease Synonyms Acute febrile neutrophilic dermatosis Ostra neutrofilowa dermatoza gorączkowa ORPHA code 3243 OMIM code 608068 ICD10 code L98.2 ICD11 code EB20 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl