Sweet syndrome

Orpha code: 3243OMIM code: 608068

Definicja

A rare inflammatory disease characterized by abrupt appearance of painful, edematous and erythematous papules, plaques and nodules on the skin, and frequently accompanied by fever and neutrophilia with a dense infiltration of mature neutrophils that are typically located in the upper dermis. The disease is classically associated with inflammatory disease, pregnancy, infection (mostly of the upper respiratory tract), or vaccination but may be idiopathic, associated with a hematological or visceral malignancy, or drug-induced.

Disease data
Klasyfikacja

Disease

Synonimy
Acute febrile neutrophilic dermatosis
Ostra neutrofilowa dermatoza gorączkowa
Kod ORPHA
3243
Kod OMIM
608068
Kod ICD10
L98.2
Kod ICD11
EB20

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl