Pleomorphic liposarcoma

Orpha code: 99969OMIM code:

Definition

Pleomorphic liposarcoma (PLS), the rarest subtype of liposarcoma (LS; see this term), is an aggressive, fast growing tumor located usually in the deep soft tissues of the lower and upper extremities. It is characterized by a variable number of pleomorphic lipoblasts and, in contrast to dedifferentiated liposarcoma, it lacks any association with well-differentiated liposarcoma (see these terms).

Disease data
Classification

Histopathological subtype

Synonyms
PLS
plS
ORPHA code
99969
OMIM code
-
ICD10 code
C49.9
ICD11 code
XH25R1

No additional description.

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