ACTH-independent Cushing syndrome

Orpha code: 99893OMIM code:

Definition

A form of endogenous Cushing syndrome (CS) that may result from excess secretion of cortisol by either a unilateral and benign (adrenocortical adenoma: 55-60%) or malignant (adrenocortical carcinoma: 35-40 %) adrenocortical tumor or by bilateral adrenal secretion by macronodular adrenal hyperplasia (AIMAH), as an isolated disease or as part of McCune-Albright syndrome (MAS), or by primary pigmented nodular adrenocortical disease (PPNAD), as an isolated disease or as part of Carney complex (CNC).

Disease data
Classification

Clinical group

Synonyms
Adrenal Cushing syndrome
Nadnerczowy zespół Cushinga
Zespół Cushinga niezależny od hormonu adrenokortykotropowego
Zespół Cushinga niezależny od kortykotropiny
Adrenocorticotropic hormone-independent Cushing syndrome
Corticotropin-independent Cushing syndrome
ORPHA code
99893
OMIM code
-
ICD10 code
E24.8
ICD11 code
-

No additional description.

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