Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A form of endogenous Cushing syndrome (CS) caused by abnormal production of ACTH due, in 80% of cases, to adrenocorticotropic hormone (ACTH) oversecretion by a pituitary adenoma (Cushing disease, CD) and in 20% of cases to ectopic ACTH secretion (CS due to EAS) by an extrapituitary tumor (in 50% of cases originating in the lungs or less commonly in the thymus, pancreas, adrenal gland or thyroid) or very rarely due to a tumor secreting both ACTH and corticotrophin-releasing hormone (CRH). Disease data Classification Clinical group Synonyms ACTH-dependent CS CS zależny od ACTH Zespół Cushinga zależny od hormonu adrenokortykotropowego Zespół Cushinga zależny od kortykotropiny Adrenocorticotropic hormone-dependent Cushing syndrome Corticotropin-dependent Cushing syndrome ORPHA code 99892 OMIM code - ICD10 code E24.0 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl