Pleuro-pericardial cyst

Orpha code: 99131OMIM code:

Definition

Pleuro-pericardial cyst is a rare, mostly congenital, pericardium anomaly characterized by the presence of, usually asymptomatic, cysts which are typically located in the right costophrenic angle and are usually incidentally diagnosed. On occasion, it manifests with chest pain, dyspnea, tachycardia, persistent cough or cardiac arrhythmias. The condition is usually benign, but rare complications, such as cardiac tamponade, cardiogenic shock, mitral valve prolapse, hoarseness atrial fibrillation, right ventricular outflow, tract obstruction, spontaneous internal hemorrhage, pulmonary stenosis and sudden death, may occur.

Disease data
Classification

Morphological anomaly

ORPHA code
99131
OMIM code
-
ICD10 code
Q24.8
ICD11 code
-

No additional description.

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