Congenital total pulmonary venous return anomaly

Orpha code: 99125OMIM code: 106700

Definition

A form of congenital pulmonary venous return where all of the pulmonary veins drain into the right atrium or one of its tributaries, instead of the left atrium, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive congestive heart failure.

Disease data
Classification

Morphological anomaly

ORPHA code
99125
OMIM code
106700
ICD10 code
Q26.2
ICD11 code
LA86.20

No additional description.

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