Congenital total pulmonary venous return anomaly

Orpha code: 99125OMIM code: 106700

Definicja

A form of congenital pulmonary venous return where all of the pulmonary veins drain into the right atrium or one of its tributaries, instead of the left atrium, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive congestive heart failure.

Disease data
Klasyfikacja

Morphological anomaly

Kod ORPHA
99125
Kod OMIM
106700
Kod ICD10
Q26.2
Kod ICD11
LA86.20

No additional description.

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