Absence of innominate vein

Orpha code: 99112OMIM code:

Definicja

A rare congenital anomaly of the great veins characterized by absence of the left brachiocephalic vein (or innominate vein), resulting in an anomalous venous vasculature. Patients are usually asymptomatic and the anomaly is typically discovered intraoperatively. An association with persistence of left superior vena cava, permanent levoatrial cardinal vein or anomaly of the inferior vena cava has been reported in some cases.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Absence of brachiocephalic vein
Brak żyły ramienno-głowowej
Kod ORPHA
99112
Kod OMIM
-
Kod ICD10
Q26.8
Kod ICD11
-

No additional description.

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