Interventricular septum aneurysm

Orpha code: 99092OMIM code: 105805

Definition

Interventricular septum aneurysm is a rare, non-syndromic, congenital heart malformation characterized by the presence of a congenital aneurysm of the membranous portion of the interventricular septum. Patients may be asymptomatic or may present with ventricular or supraventricular tachycardia, fatigue, exertional dyspnea, palpitations, and cardiac murmur. Ventricular septal defects and conduction defects, such as first-degree atrio-ventricular block or incomplete right bundle branch block, may also be also associated.

Disease data
Classification

Morphological anomaly

ORPHA code
99092
OMIM code
105805
ICD10 code
Q21.0
ICD11 code
-

No additional description.

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