Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare coronary artery congenital malformation characterized by congenital, partial or total occlusion of the left or right coronary artery orifice, associated with hypoplasia of the proximal segment of the corresponding coronary artery. It may present with failure to thrive, dyspnea, syncope, angina pectoris, ventricular tachycardia, myocardial ischemia and/or sudden death. Disease data Classification Morphological anomaly Synonyms COSA Congenital coronary arterial orifice stenosis or atresia Congenital stenosis or atresia of a coronary ostium COSA Congenital coronary arterial orifice stenosis or atresia Congenital stenosis or atresia of a coronary ostium ORPHA code 99087 OMIM code - ICD10 code Q24.5 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl