Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare, congenital anomaly of the great arteries characterized by various clinical signs and symptoms, shortness of breath, including recurrent lower respiratory tract infections, lung hypoplasia, pulmonary hypertension, and haemoptysis. The anomaly can be isolated or associated with congenital heart disease, such as tetralogy of Fallot, atrial septal defect, coarctation of the aorta, right aortic arch, truncus arteriosus, patent ductus arteriosus and pulmonary atresia. Disease data Classification Morphological anomaly Synonyms PAH Unilateral Pulmonary Artery Hypoplasia PAH Unilateral Pulmonary Artery Hypoplasia ORPHA code 99083 OMIM code - ICD10 code Q25.7 ICD11 code LA8B.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl