Congenital anomaly of the tricuspid valve chordae

Orpha code: 99055OMIM code:

Definicja

A rare, congenital anomaly of the tricuspid subvalvular apparatus characterized by aberrant tendinous chords, which insert at the clear zone of the leaflet instead of its free edge and connect to the endocardium instead of the papillary muscles. Resulting tethering of one or more tricuspid leaflets leads to their impaired mobility and tricuspid regurgitation. Association with other congenital cardiac anomalies has been reported.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Congenital anomaly of tricuspid chordae tendineae
Congenital anomaly of tricuspid tendinous chords
Congenital anomaly of tricuspid chordae tendineae
Congenital anomaly of tricuspid tendinous chords
Kod ORPHA
99055
Kod OMIM
-
Kod ICD10
Q22.8
Kod ICD11
-

No additional description.

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