Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare, congenital anomaly of the tricuspid subvalvular apparatus characterized by aberrant tendinous chords, which insert at the clear zone of the leaflet instead of its free edge and connect to the endocardium instead of the papillary muscles. Resulting tethering of one or more tricuspid leaflets leads to their impaired mobility and tricuspid regurgitation. Association with other congenital cardiac anomalies has been reported. Disease data Classification Morphological anomaly Synonyms Congenital anomaly of tricuspid chordae tendineae Congenital anomaly of tricuspid tendinous chords Congenital anomaly of tricuspid chordae tendineae Congenital anomaly of tricuspid tendinous chords ORPHA code 99055 OMIM code - ICD10 code Q22.8 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl