Mast cell leukemia

Orpha code: 98851OMIM code:

Definicja

A very rare malignant systemic mastocytosis (SM) characterized by a huge infiltration of bone marrow, and often of blood, by abnormal mast cells (MC) which frequently manifests with organ dysfunction (liver, spleen, peritoneum, bones, and marrow).

Disease data
Klasyfikacja

Disease

Kod ORPHA
98851
Kod OMIM
-
Kod ICD10
C94.3
Kod ICD11
2A21.00

No additional description.

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