Aggressive systemic mastocytosis

Orpha code: 98850OMIM code:

Definicja

A rare, aggressive form of advanced systemic mastocytosis (advSM) characterized by massive infiltration of mast cells (MC) in different tissues and presence of extracutaneous organ dysfunction, but without evidence of mast cell leukemia or another hematologic neoplasm.

Disease data
Klasyfikacja

Disease

Kod ORPHA
98850
Kod OMIM
-
Kod ICD10
C96.2
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl