Indolent systemic mastocytosis

Orpha code: 98848OMIM code:

Definition

A rare, usually benign, chronic, form of systemic mastocytosis (SM) characterized by an abnormal accumulation of neoplastic mast cells (MCs) mainly in the bone marrow (BM) but also in other organs or tissues such as preferably the skin.

Disease data
Classification

Disease

ORPHA code
98848
OMIM code
-
ICD10 code
D47.0
ICD11 code
-

No additional description.

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