Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare subtype of diffuse large B-cell lymphoma (DLBCL), arising from B cells of thymic origin, predominantly affecting women between the ages of 20-30, and that usually presents with a bulky and rapidly expanding anterior mediastinal mass, often with pleural and pericardial effusions, and that can invade the lungs, superior vena cava, pleura, pericardium, and chest wall, leading to manifestations of cough, dyspnea, and superior vena cava syndrome. Disease data Classification Disease Synonyms Large cell lymphoma of the mediastinum Chłoniak wielkokomórkowy śródpiersia Med-DLBCL Pierwotny chłoniak jasnokomórkowy śródpiersia z komórek B Rozlany chłoniak wielkokomórkowy śródpiersia ze sklerozą Med-DLBCL Mediastinal diffuse large-cell lymphoma with sclerosis Primary mediastinal clear cell lymphoma of B-cell type ORPHA code 98838 OMIM code - ICD10 code C83.3 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl