Primary mediastinal large B-cell lymphoma

Orpha code: 98838OMIM code:

Definition

A rare subtype of diffuse large B-cell lymphoma (DLBCL), arising from B cells of thymic origin, predominantly affecting women between the ages of 20-30, and that usually presents with a bulky and rapidly expanding anterior mediastinal mass, often with pleural and pericardial effusions, and that can invade the lungs, superior vena cava, pleura, pericardium, and chest wall, leading to manifestations of cough, dyspnea, and superior vena cava syndrome.

Disease data
Classification

Disease

Synonyms
Large cell lymphoma of the mediastinum
Chłoniak wielkokomórkowy śródpiersia
Med-DLBCL
Pierwotny chłoniak jasnokomórkowy śródpiersia z komórek B
Rozlany chłoniak wielkokomórkowy śródpiersia ze sklerozą
Med-DLBCL
Mediastinal diffuse large-cell lymphoma with sclerosis
Primary mediastinal clear cell lymphoma of B-cell type
ORPHA code
98838
OMIM code
-
ICD10 code
C83.3
ICD11 code
-

No additional description.

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