Benign childhood occipital epilepsy, Panayiotopoulos type

Orpha code: 98815OMIM code:

Definition

Benign childhood occipital epilepsy, Panayiotopoulos type is a rare, genetic neurological disorder characterized by late infancy to early-adolescence onset of prolonged, nocturnal seizures which begin with autonomic features (e.g. vomiting, pallor, sweating) and associate tonic eye deviation, impairment of consciousness and may evolve to a hemi-clonic or generalized convulsion. Autonomic status epilepticus may be the only clinical event in some cases.

Disease data
Classification

Clinical subtype

Synonyms
Early-onset benign childhood occipital epilepsy
Łagodna dziecięca padaczka potyliczna, typ Panayiotopoulosa
Panayiotopoulos syndrome
ORPHA code
98815
OMIM code
-
ICD10 code
G40.0
ICD11 code
-

No additional description.

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