Congenital trochlear nerve palsy

Orpha code: 98686OMIM code:

Definicja

A rare ophthalmic disorder with cranial nerve involvement characterized by dysfunction of the superior oblique muscle with typical eye motility patterns including elevation in adduction, V-pattern related to reduced abduction force in downgaze with unopposed adduction by the inferior rectus muscle, and excyclotorsion. Patients may present with contralateral head tilt to compensate for vertical binocular misalignment and diplopia.

Disease data
Klasyfikacja

Disease

Synonimy
Congenital CNIV palsy
Wrodzone porażenie CNIV
Wrodzone porażenie czwartego nerwu czaszkowego
Congenital fourth cranial nerve palsy
Congenital superior oblique palsy
Kod ORPHA
98686
Kod OMIM
-
Kod ICD10
H49.1
Kod ICD11
-

No additional description.

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