Testicular regression syndrome

Orpha code: 983OMIM code: 273250

Definicja

Testicular regression syndrome (TRS) is a developmental anomaly characterized by the absence of one or both testicles with partial or complete absence of testicular tissue. TRS may vary from normal male with unilateral no-palpable testis through phenotypic male with micropenis, to phenotypic female. The phenotype depends on the extent and timing of the intrauterine accident in relation to sexual development.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
ETRS
Embrionalny zespół regresji jąder
ETRS
TRS
Zespół zanikających jąder
Embryonic testicular regression syndrome
TRS
Vanishing testes syndrome
Vanishing testis syndrome
XY gonadal agenesis syndrome
Kod ORPHA
983
Kod OMIM
273250
Kod ICD10
Q55.0
Kod ICD11
LD2A.Y

No additional description.

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