Testicular regression syndrome

Orpha code: 983OMIM code: 273250

Definition

Testicular regression syndrome (TRS) is a developmental anomaly characterized by the absence of one or both testicles with partial or complete absence of testicular tissue. TRS may vary from normal male with unilateral no-palpable testis through phenotypic male with micropenis, to phenotypic female. The phenotype depends on the extent and timing of the intrauterine accident in relation to sexual development.

Disease data
Classification

Morphological anomaly

Synonyms
ETRS
Embrionalny zespół regresji jąder
ETRS
TRS
Zespół zanikających jąder
Embryonic testicular regression syndrome
TRS
Vanishing testes syndrome
Vanishing testis syndrome
XY gonadal agenesis syndrome
ORPHA code
983
OMIM code
273250
ICD10 code
Q55.0
ICD11 code
LD2A.Y

No additional description.

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