Non-amyloid fibrillary glomerulopathy

Orpha code: 97566OMIM code:

Definition

Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy (ITG, see this term) are often grouped together as pathogenetically related diseases.

Disease data
Classification

Disease

Synonyms
Congo red-negative amyloidosis-like glomerulopathy
Non-amyloid fibrillary glomerulonephritis
Congo red-negative amyloidosis-like glomerulopathy
Non-amyloid fibrillary glomerulonephritis
ORPHA code
97566
OMIM code
-
ICD10 code
N03.6
ICD11 code
-

No additional description.

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