Bilateral multicystic dysplastic kidney

Orpha code: 97364OMIM code:

Definicja

A rare lethal form of multicystic dysplastic kidney (MCDK), a congenital anomaly of the kidney and urinary tract (CAKUT), in which both kidneys are large, distended by non-communicating multiple cysts and non-functional.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Bilateral MCDK
Obustronna MCDK
Obustronna wielotorbielowata dysplazja nerki
Bilateral multicystic renal dysplasia
Kod ORPHA
97364
Kod OMIM
-
Kod ICD10
Q61.4
Kod ICD11
-

No additional description.

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