Accessory tricuspid valve tissue

Definition

A rare, congenital, atrioventricular valve malformation characterized by fixed or mobile accessory tissue on the tricuspid valve, usually associated with other complex congenital heart anomalies (atrial septal defect, ventricular septal defect, transposition of great arteries, tetralogy Fallot). It may present clinically with systolic murmur, dyspnea, cyanosis, depending also on accompanying congenital heart anomaly.

Disease data

Classification

Morphological anomaly

ORPHA code

95462

OMIM code

ICD10 code

Q22.8

ICD11 code

*Soruce