Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare, congenital, non-syndromic heart malformation characterized by partial or complete absence of tricuspid valve tissue and its apparatus, with an existing orifice. It can be isolated or associated with other heart anomalies. Clinical presentation is variable and may include syncope, arrhythmias, cyanosis, right heart dilatation and failure. Disease data Classification Morphological anomaly Synonyms Congenital unguarded tricuspid orifice Wrodzony brak zastawki trójdzielnej ORPHA code 95457 OMIM code - ICD10 code Q22.4 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl