Tricuspid valve agenesis

Orpha code: 95457OMIM code:

Definicja

A rare, congenital, non-syndromic heart malformation characterized by partial or complete absence of tricuspid valve tissue and its apparatus, with an existing orifice. It can be isolated or associated with other heart anomalies. Clinical presentation is variable and may include syncope, arrhythmias, cyanosis, right heart dilatation and failure.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Congenital unguarded tricuspid orifice
Wrodzony brak zastawki trójdzielnej
Kod ORPHA
95457
Kod OMIM
-
Kod ICD10
Q22.4
Kod ICD11
-

No additional description.

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