Primary progressive aphasia

Orpha code: 95432OMIM code:

Definicja

Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD; see this term) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA) (see these terms).

Disease data
Klasyfikacja

Clinical group

Synonimy
Mesulam syndrome
PPA
Zespół Mesulama
PPA
Kod ORPHA
95432
Kod OMIM
-
Kod ICD10
G31.0
Kod ICD11
6D83

No additional description.

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