Primary progressive aphasia

Orpha code: 95432OMIM code:

Definition

Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD; see this term) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA) (see these terms).

Disease data
Classification

Clinical group

Synonyms
Mesulam syndrome
PPA
Zespół Mesulama
PPA
ORPHA code
95432
OMIM code
-
ICD10 code
G31.0
ICD11 code
6D83

No additional description.

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