Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition An early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder with vasculopathy, characterized by proximal and symmetrical muscle weakness, evocative skin lesions, and systemic manifestations. Vasculopathy occurs in the skin, muscle (mainly in the perifascicular area), and sometimes in the intestinal tissue. Disease data Classification Disease Synonyms Juvenile DM Młodzieńcze DM ORPHA code 93672 OMIM code - ICD10 code M33.0 ICD11 code 4A41.01 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl