Renal dysplasia, unilateral

Orpha code: 93172OMIM code:

Definition

A form of renal dysplasia (RD) characterized by abnormal or incomplete development of one kidney. Unilateral RD can be segmental, and of variable severity, with renal aplasia corresponding to extreme RD. Patients may be asymptomatic if the contralateral kidney is functional. Even in cases of severe unilateral RD, i.e. renal aplasia, the risk of renal failure in childhood is minimal; however, patients may develop hypertension, proteinuria and renal failure as adults.

Disease data
Classification

Clinical subtype

Synonyms
Kidney dysplasia, unilateral
Kidney dysplasia, unilateral
ORPHA code
93172
OMIM code
-
ICD10 code
Q61.4
ICD11 code
-

No additional description.

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