Renal dysplasia, unilateral

Orpha code: 93172OMIM code:

Definicja

A form of renal dysplasia (RD) characterized by abnormal or incomplete development of one kidney. Unilateral RD can be segmental, and of variable severity, with renal aplasia corresponding to extreme RD. Patients may be asymptomatic if the contralateral kidney is functional. Even in cases of severe unilateral RD, i.e. renal aplasia, the risk of renal failure in childhood is minimal; however, patients may develop hypertension, proteinuria and renal failure as adults.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Kidney dysplasia, unilateral
Kidney dysplasia, unilateral
Kod ORPHA
93172
Kod OMIM
-
Kod ICD10
Q61.4
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl