Primary intestinal lymphangiectasia

Orpha code: 90362OMIM code: 152800

Definition

A rare intestinal disease characterized by dilated intestinal lacteals which cause lymph leakage into the small bowel lumen. Clinical manifestations include edema related to hypoalbuminemia (protein-losing gastro-enteropathy), asthenia, moderate diarrhea, lymphedema, serous effusion and failure to thrive in children.

Disease data
Classification

Disease

Synonyms
Waldmann disease
Choroba Waldmanna
ORPHA code
90362
OMIM code
152800
ICD10 code
I89.0
ICD11 code
-

No additional description.

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