Primary intestinal lymphangiectasia

Orpha code: 90362OMIM code: 152800

Definicja

A rare intestinal disease characterized by dilated intestinal lacteals which cause lymph leakage into the small bowel lumen. Clinical manifestations include edema related to hypoalbuminemia (protein-losing gastro-enteropathy), asthenia, moderate diarrhea, lymphedema, serous effusion and failure to thrive in children.

Disease data
Klasyfikacja

Disease

Synonimy
Waldmann disease
Choroba Waldmanna
Kod ORPHA
90362
Kod OMIM
152800
Kod ICD10
I89.0
Kod ICD11
-

No additional description.

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