Hepatic veno-occlusive disease

Orpha code: 890OMIM code:

Definition

A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites.

Disease data
Classification

Disease

Synonyms
Sinusoidal obstruction syndrome
Zespół niedrożności zatok wątrobowych
ORPHA code
890
OMIM code
-
ICD10 code
K76.5
ICD11 code
DB98.6

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl