Alport syndrome-intellectual disability-midface hypoplasia-elliptocytosis syndrome

Orpha code: 86818OMIM code: 300990

Definicja

A rare constitutional hemolytic anemia that is characterised by the association of Alport syndrome, midface hypoplasia, intellectual deficit and elliptocytosis. It has been described in two families. The syndrome is transmitted as an X-linked trait is caused by a contiguous gene deletion in Xq22.3 involving several genes including <i>COL4A5</i>, <i>FACL4</i> and <i>AMMECR1</i>.

Disease data
Klasyfikacja

Disease

Synonimy
AMME complex
ATS-MR
Kompleks AMME
Zespół AMME
AMME syndrome
ATS-MR
Kod ORPHA
86818
Kod OMIM
300990
Kod ICD10
Q87.8
Kod ICD11
-

No additional description.

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