Craniometadiaphyseal dysplasia, wormian bone type

Orpha code: 85184OMIM code: 269300

Definicja

Craniometadiaphyseal dysplasia, wormian bone type is an extremely rare craniotubular bone dysplasia syndrome described in fewer than 10 patients to date. Clinical manifestations include macrocephaly, frontal bossing, malar hypoplasia, prominent mandible and dental hypoplasia. Other skeletal anomalies include abnormal bone modeling in tubular bones, multiple wormian bones and deformities of chest, pelvis and elbows. An increased risk of fractures is noted.

Disease data
Klasyfikacja

Malformation syndrome

Kod ORPHA
85184
Kod OMIM
269300
Kod ICD10
Q78.8
Kod ICD11
-

No additional description.

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