Collagen type III glomerulopathy

Orpha code: 84087OMIM code:

Definicja

A rare non-immune-mediated glomerular disease characterized by abnormal accumulation of type III collagen within the mesangium and subendothelial space of the glomerulus. Clinically it usually manifests with proteinuria (often in the nephrotic range), microscopic hematuria, peripheral edema and/or hypertension. Progression to end-stage kidney failure is possible.

Disease data
Klasyfikacja

Disease

Synonimy
Collagenofibrotic glomerulopathy
Collagenofibrotic glomerulopathy
Kod ORPHA
84087
Kod OMIM
-
Kod ICD10
N07.6
Kod ICD11
-

No additional description.

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